Anomalous origin of left coronary artery from the pulmonary artery syndrome : A case report
Anomalous origin of left coronary artery from the pulmonary artery syndrome ,is a rare congenital cardiac anomaly.
The majority of patients die within first year of life if left untreated. However ,a few patients can be asymptomatic and survive into adulthood due to well-developed collateral between left coronary artery and dilated right coronary artery.
We reported a case of a 17 years old male who has been had faint symptom working in quarry. Presented with sudden death and his autopsy revealed ALCAPA syndrome with dilated right coronary artery.
Anomalous origin of the left coronary artery (LCA) from the pulmonary artery (ALCAPA) is a rare congenital anomaly that commonly presents in infancy occurring in approximately 1/ 300,000 live births , which if untreated has up to 85% mortality, most deaths occurring before 1 year of age from complications related to heart failure, Some patients remain asymptomatic likely secondary to an extensive network of collateral vessels between ther ight and left coronary system.
The small minority of patients who survive to adulthood with ALCAPA will ultimately develop symptoms, or present with arrhythmia, syncope or sudden death